Hepatic manifestations of cystic fibrosis
Cystic fibrosis (CF) is the most common autosomal recessive genetic disorder in white
people, 1, 2 and is also one of the most lethal. 3, 4 It is caused by a mutation in the gene
coding for the CF transmembrane conductance regulator (CFTR) protein on chromosome 7.
2 With advances in medical care, the life expectancy of patients with CF has increased from
16 years in 1970 to 47.7 years in 2016. 5 Given this improved longevity,
people, 1, 2 and is also one of the most lethal. 3, 4 It is caused by a mutation in the gene
coding for the CF transmembrane conductance regulator (CFTR) protein on chromosome 7.
2 With advances in medical care, the life expectancy of patients with CF has increased from
16 years in 1970 to 47.7 years in 2016. 5 Given this improved longevity,